2006, Number 2
Intestinal Pseudo Obstruction in Newborn Visceral Myopathy. A Case Report
Peniche-García R, Rodriguez-Moguel L
Full text
Language: Spanish
References: 10
Page: 87-91
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ABSTRACT
Background: Abnormalities of smooth muscle interested the entire digestive tract and may affect other organs, particularly the urinary tract. Visceral myopathy belongs to a group of clinical entities characterized by deficiency in intestinal motility and represents the most common cause of primary intestinal pseudoobstruction as initial presentation may mimic an intestinal atresia box. Due to the difficulty of diagnosis, patient outcome and especially the need to provide an early prognosis decided to communicate this case.Clinical Case Presentation: This is a young mother female patient with history of antiphospholipid syndrome and suffer from prenatal ultrasound was detected hydronephrosis and megacystis. Abdomen were taken appreciating Rx dilated stomach and images suggestive of intestinal atresia. She underwent exploratory laparotomy intestinal obstruction by meconium finding difficult to extract taffy.
The postoperative course was poor and did not reestablish the intestinal transit at 10 days is finding a bladder reoperate reaching to the xiphoid, and bridles little dilatation proximal to the anastomosis. We practice a second bowel resection anastomosis now vesocostomía iliocólica and skin. The pathology report was both visceral myopathy and intestinal bladder wall. Never re-established intestinal transit, until the 70 days of life passed
Discussion: The report of a prenatal ultrasound megacystis gastric dilation and should make us think about the possibility of this syndrome Megacistis, microcolon and hipoteristalsis which mainly affects female neonates whose clinical presentation is an intestinal pseudo-obstruction in general terms not benefit from an operation and will require supportive measures such as parenteral nutrition and the prognosis is almost always fatal in the short term although there are reports of survivors from a few years but with very poor quality of life.
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