2012, Number 1
Neurofibroma of the pancreas: unusual presentation in a patient at Hospital Infantil de Mexico Federico Gomez
González FL, Romero BBL, Valadez RMT, Dies SP, Sarmiento AMA, Flores AEM
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ABSTRACTWe present the case of a patient age 18 years, carrier of type 1 neurofibromatosis, in whom a lesion in the popliteal fossa was detected with histopathological diagnosis of neurofibroma. Image follow-up detected a hypoechoic lesion in uncinate process and pancreatic head. The subject subsequently experienced three months of abdominal pain, and growth of the lesion with heterogeneous echotexture was observed in the follow-up ultrasound. The subject underwent surgical treatment, and histopathological diagnosis found a malignant peripheral nerve sheath tumor originating in a plexiform neurofibroma with compromise of the cecal appendix and peritoneum. The age of appearance and location of the lesion are the main points of interest in this clinical case.