Pérez-Elizondo AD, Ruiz-Pérez ME, Gutiérrez CME

Language: Spanish
References: 10
Page: 27-29
PDF size: 289.19 Kb.

ABSTRACT

First described in 1880, known as calcifying epitelioma of sebaceous glands, calcifying epitelioma of Malherbe or pilomatrixoma. It is a rare benign adnexal tumor derived from cells of the matrix and hairy cortex, asymptomatic, in patients from 8 to 13 years of age, female, slow-growing, painless, irregular borders, of between 0.5 mm to 5 cm. Diagnosis is clinical and confirmed by histologic examination and treatment is usually surgical. Recurrences are rare but should be suspected to present a variant of malignant pilomatrixoma. We report the case of a three-year-old with painless cutaneous neoplasm in right cheek approach and interpretation difficult medical-diagnostic corresponding to a pilomatrixoma with clinicopathologic correlation. Was completely removed without recurrence in subsequent control visits. The importance of the case lies in the correct clinical identification of such relatively rare tumors in pediatric practice.

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