2019, Number 3
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Rev Med MD 2019; 10.11 (3)
Myelod Sarcoma: an uncommon entity
Rodríguez-Bautista E, Méndez-González A, Martínez-Coronel J
Language: Spanish
References: 10
Page: 245-249
PDF size: 603.04 Kb.
ABSTRACT
Myeloid Sarcoma (MS), also called Acute Extramedullary Myeloid Leukemia, Extramedullary Myeloid Tumor or
Granulocytic Sarcoma, is a rare neoplastic condition characterized by the appearance of one or more tumor masses,
consisting of immature myeloid cells in an extramedullary site, commonly arising in the skin, bone or lymph nodes,
although it can appear anywhere in the body.
We present the case of a 39-year-old male patient with cutaneous clinical manifestation, nocturnal diaphoresis and
intermittent fever.
MS occurs more frequently in association with Acute Myeloid Leukemia (AML), affecting 2.5 to 9.1% of these
patients; When it is detected before the clinical signs of leukemia and in association with a normal bone marrow biopsy
is described as primary or isolated MS, this rare pathology has an incidence of 2/1 000 000 in the adult population,
thus, the clinical and pathological diagnosis can be a challenge.
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