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>Journals >Cirujano General >Year 2004, Issue 4

Mondragón SA, Mondragón SR, Alvear M, Bernal MR, Mondragón BR
Inter-aorto-cava retroperitoneal paraganglioma
Cir Gen 2004; 26 (4)

Language: Español
References: 20
Page: 325-329
PDF: 4. Kb.

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Introduction: Paragangliomas are tumors originated from the chromaffin cells of the neural crest. They can be observed from the base of the skull to the bladder or along the sympathetic ganglionar chain. Retroperitoneal paragangliomas can represent a true surgical challenge due to their tight relation to large size vessels. Presentation of the case: Woman, of 40 years of age, who, three years before admittance, had presented paroxysmal crises of severe arterial hypertension. The abdominal TC scan revealed the presence of an inter-aorto-cava retroperitoneal mass of 4 cm in diameter compatible with a paraganglioma. The patient was subjected to surgery after having been prepared with calcium channel blockers during two weeks. Surgery confirmed the presence of the inter-aorto-cava paranganglioma of 5 cm in diameter that displaced the cava vein to the front; the tumor was successfully resected. The patient required intensive care and was discharged on the 7th day after surgery without complications. At 24 months, her blood pressure is normal and without recurrence. Conclusion: Retroperitoneal paragangliomas are not frequent tumors, their surgical treatment is difficult. A multidisciplinary specialized team and close monitoring during the perioperative period are required.

Key words: Paranganglioma, retroperitoneum.


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>Journals >Cirujano General >Year 2004, Issue 4

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