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ISSN 2539-0859 (Electronic)
ISSN 0120-8411 (Print)
Asociación Colombiana de Otorrinolaringología y Cirugía de Cabeza y cuello, Maxilofacial y Estética Facial (ACORL)

2022, Number 4

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Acta de Otorrinolaringología CCC 2022; 50 (4)

Nasal ala Alveolar Rhabdomyosarcoma in a pediatric patient. A rare case report

Olivera-Arenas MP, Romero-Moreno LF, Marrugo-Pardo GE, Tavera-Cordero J

Language: Spanish
References: 18
Page: 300-303
PDF size: 199.40 Kb.


ABSTRACT

Given preferential nasal breathing in the first months of life in the pediatric population, nasal obstruction has more clinical repercussions than it would have in adults, hence the need to give higher priority to its diagnosis and management. One of the main causes of nasal obstruction in children is the presence of nasal masses, which cause considerable diagnostic uncertainty in the medical team, because of their multiple etiologies. In this article, the case of a 10-month-old patient with a rapidly growing mass in the nasal ala is presented. A rhabdomyosarcoma was promptly diagnosed and adequately managed. Rhabdomyosarcoma with an alveolar pattern occurs in an unusual way in this location; for this reason, this case is important in order to include this possibility in the diagnostic algorithm and, as was the case in this patient, reach an early diagnosis and institute adequate treatment resulting in favorable aesthetic and functional results.


REFERENCES

  1. Miettinen M. Small round cell tumor. In: Soft tissue tumors.Philadelphia: Churchill-Livingston; 2003. p. 427-62.

  2. Bridge JA, Bowen JM, Smith RB. The small round blue celltumors of the sinonasal area. Head Neck Pathol. 2010;4(1):84-93. doi: 10.1007/s12105-009-0158-6

  3. Gnagi SH, Schraff SA. Nasal obstruction in newborns.Pediatr Clin North Am. 2013;60(4):903-22. doi: 10.1016/j.pcl.2013.04.007

  4. Leboulanger N. Nasal obstruction in children. Eur AnnOtorhinolaryngol Head Neck Dis. 2016;133(3):183-6. doi:10.1016/j.anorl.2015.09.011

  5. Kinshucka AJ, Clark RW. Nasal masses in children. TheOtorhinolaryngologist. 2012;5(3):133-38.

  6. Chung SY, Unsal AA, Kılıç S, Baredes S, Liu JK, Eloy JA.Pediatric sinonasal malignancies: A population-based analysis.Int J Pediatr Otorhinolaryngol. 2017;98:97-102. doi: 10.1016/j.ijporl.2017.04.032

  7. Tanyous GH. Rhabdomyosarcoma of the nasal vestibule in achild. Sultan Qaboos Univ Med J. 2006;6(2):87-9.

  8. Hicks J, Flaitz C. Rhabdomyosarcoma of the head and neckin children. Oral Oncol. 2002;38(5):450-9. doi: 10.1016/s1368-8375(01)00105-1

  9. Radzikowska J, Kukwa W, Kukwa A, Czarnecka A, Krzeski A.Rhabdomyosarcoma of the head and neck in children. ContempOncol (Pozn). 2015;19(2):98-107. doi: 10.5114/wo.2015.49158

  10. Sung L, Anderson JR, Arndt C, Raney RB, Meyer WH, PappoAS. Neurofibromatosis in children with Rhabdomyosarcoma:a report from the Intergroup Rhabdomyosarcoma study IV. JPediatr. 2004;144(5):666-8. doi: 10.1016/j.jpeds.2004.02.026

  11. Carnevale A, Lieberman E, Cárdenas R. Li-Fraumeni syndromein pediatric patients with soft tissue sarcoma or osteosarcoma.Arch Med Res. 1997 Autumn;28(3):383-6.

  12. O’Neal JP, Ramdas J, Wood WE, Pellitteri PK. Parameningealrhabdomyosarcoma in a patient with Costello syndrome.J Pediatr Hematol Oncol. 2004;26(6):389-92. doi:10.1097/00043426-200406000-00012

  13. Jung A, Bechthold S, Pfluger T, Renner C, Ehrt O. Orbitalrhabdomyosarcoma in Noonan syndrome. J Pediatr HematolOncol. 2003;25(4):330-2. doi: 10.1097/00043426-200304000-00014

  14. Smith AC, Squire JA, Thorner P, Zielenska M, Shuman C,Grant R, et al. Association of alveolar rhabdomyosarcomawith the Beckwith-Wiedemann syndrome. Pediatr Dev Pathol.2001;4(6):550-8. doi: 10.1007/s10024001-0110-6

  15. Arndt CA. Risk stratification of rhabdomyosarcoma: a movingtarget. Am Soc Clin Oncol Educ Book. 2013:415-9. doi:10.14694/EdBook_AM.2013.33.415

  16. Arndt CA, Stoner JA, Hawkins DS, Rodeberg DA, Hayes-Jordan AA, Paidas CN, et al. Vincristine, actinomycin, andcyclophosphamide compared with vincristine, actinomycin, andcyclophosphamide alternating with vincristine, topotecan, andcyclophosphamide for intermediate-risk rhabdomyosarcoma:children’s oncology group study D9803. J Clin Oncol.2009;27(31):5182-8. doi: 10.1200/JCO.2009.22.3768

  17. Oberlin O, Rey A, Lyden E, Bisogno G, Stevens MC, MeyerWH, et al. Prognostic factors in metastatic rhabdomyosarcomas:results of a pooled analysis from United States and Europeancooperative groups. J Clin Oncol. 2008;26(14):2384-9. doi:10.1200/JCO.2007.14.7207

  18. Parham DM, Barr FG. Alveolar rhabdomyosarcoma. In:Fletcher CDM, Unni KK, Mertens F, eds. Pathology andGenetics of Tumours of Soft Tissue and Bone. Lyon: IARCPress; 2002. p. 150-52.




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