Soriano MJL, Maldonado RCA, Pérez MA, Cervantes GJE, Robles GJA

Language: Spanish
References: 11
Page: 36-41
PDF size: 419.08 Kb.

ABSTRACT

Introduction: radial polydactyly encompasses a large group of congenital malformations of the thumb, being the second most common congenital malformation of the hand with an incidence of 1 in 3,000 live births. Objective: to report the clinical case of a lactating female patient with the presence of a bilateral duplicated triphalangeal thumb, its diagnostic protocol, treatment and follow-up for one year. Clinical case: nine-month-old female patient diagnosed with bilateral Wassel VII B radial polydactyly plus ulnar syndactyly. An ulnar thumb resection with an on top plasty technique is performed as an initial surgical treatment, as well as surgical release of the syndactyly bilaterally. Two years later, triflangic thumb correction surgery was performed through a reduction, rotation and abduction osteotomy of the first metacarpal associated with a reduction osteotomy and arthrodesis of the distal interphalangeal joint bilaterally. A 1-year clinical follow-up is carried out, observing the presence of a thumb with an adequate appearance, with ranges of mobility with adequate abduction, extension, flexion and opposition, presence of a fine and thick clamp, with adequate muscle strength, preserved sensitivity bilaterally. Conclusions: polydactylies of the thumb present a very rare congenital malformation with multiple characteristics which make it difficult to make a decision regarding definitive surgical treatment, which is why an analysis of the pathological variant of the malformation and the possible causes must be carried out. types of treatment prior to its final resolution with the objective of presenting functional results and satisfactory evolution.

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EVIDENCE LEVEL

IV